Renal Primitive Neuroectodermal Tumor or Renal Ewing Sarcoma

Renal primitive neuroectodermal tumor (renal PNET) or renal Ewing sarcoma ES) is a rare, rapidly growing malignant small round cell with poor prognosis. A 32-years-old Bangladeshi male patient presented right loin pain, fever and anemia. On CT imaging large (18x10.5x10.0 cm) mass was discovered. suspicion of malignancy, biopsy taken from the mass. Microscopic evaluation showed features consistent blue tumor. Immunohistochemical stains diffuse strong positive reaction to CD-99 negative for WT-1, CD-3 CD-20, which confirmed diagnosis PNET. After 6 cycles combined chemotherapy, relatively well at months follow-up he no evidence metastasis recurrence.
 KYAMC Journal Vol. 13, No. 04, January 2023: 257-260